Many factors inhibit the reliability of the eeg data. A child with lks has a progressive loss of language abilities understanding and speaking after previously developing normally for their age. Age of onset and outcome in acquired aphasia with convulsive disorder landaukleffner. May 19, 20 the most important lesson from 83,000 brain scans daniel amen tedxorangecoast duration. Landaukleffner syndrome lksalso called infantile acquired aphasia, acquired epileptic aphasia or aphasia with convulsive disorderis a rare childhood neurological syndrome. Landau kleffner syndrome lks is a rare and underdiagnosed epilepsy syndrome. Sintomas y tratamiento del sindrome landaukleffner todopapas. In additional to language regression, the diagnosis requires the presence of severely epileptiform activity on eeg, particularly during nonrem sleep. A biopsia cerebral e os testes sorologicos dao resultados mistos e nao confirmam a. Landau kleffner syndrome nord national organization for. Aug 11, 2017 landau kleffner syndrome lks is a rare neurological syndrome characterized by the sudden or gradual development of aphasia the inability to understand or express language and recurrent seizures epilepsy. Affected siblings and discordant monozygotic twins have been reported rarely.
Tienen una actividad electrica cerebral anormal en ambos lados del cerebro. The most important lesson from 83,000 brain scans daniel amen tedxorangecoast duration. Landaukleffner syndrome lks is a rare neurological syndrome characterized by the sudden or gradual development of aphasia the inability to understand or express language and recurrent seizures epilepsy. It is named after william landau and frank kleffner, who characterized it in 1957 with a diagnosis of six children. Landau kleffner syndrome is a rare disorder that affects twice as many males as females.
Landau kleffner syndrome lks begins between 2 and 8 years of age average 5 to 7 years. These children will have developed speech normally and then, suddenly or gradually lose language skills for no apparent reason. Bishop, 1985 o afasia infantil adquirida con epilepsia. It usually occurs in children between the ages of 3 and 9 and affects the area of the brain that controls speech and comprehension. Landaukleffnersyndrom aphasie, epileptische, erworbene aphasie, erworbene epileptische erworbene dysphasie im kindesalter mit krampfanfallen. Kleffner, who identified six children with the disorder. Landaukleffner syndrome lks is a rare, childhood neurological disorder characterized by the sudden or gradual development of aphasia the inability to understand or express language and an abnormal electroencephalogram eeg. Landaukleffner syndrome is an epileptic encephalopathy characterized by acquired verbal auditory aphasia and seizures in most of the patients associated with continuous or almost continuous spikeandwave discharges during slow wave sleep. Kleffner 1957, tambien conocido como afasia adquirida con trastorno convulsivo bishop. Lks may also be called infantile acquired landaiacquired epileptic aphasia or aphasia with convulsive disorder.
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